產品編號 | bs-17348R-BF488 |
英文名稱 | Rabbit Anti-HOGA1/BF488 Conjugated antibody |
中文名稱 | BF488標記的HOGA1蛋白抗體 |
別 名 | 4 hydroxy 2 oxoglutarate aldolase 1; C10orf65; DHDPS like protein; DHDPS2; DHDPSL; Dihydrodipicolinate synthase like; Dihydrodipicolinate synthase like, mitochondrial; Dihydrodipicolinate synthetase homolog 2; FLJ37472; HOGA1; HOGA1_HUMAN; HP3; mitochondrial; N acetylneuraminate pyruvate lyase 2 (putative); NPL2; Probable 2 keto 4 hydroxyglutarate aldolase; Probable 4 hydroxy 2 oxoglutarate aldolase mitochondrial; Probable 4-hydroxy-2-oxoglutarate aldolase; Probable KHG aldolase; Protein 569272. |
規(guī)格價格 | 100ul/2980元 購買 大包裝/詢價 |
說 明 書 | 100ul |
研究領域 | 細胞生物 信號轉導 新陳代謝 |
抗體來源 | Rabbit |
克隆類型 | Polyclonal |
交叉反應 | Mouse, (predicted: Human, ) |
產品應用 | ICC=1:50-200 IF=1:50-200
not yet tested in other applications. optimal dilutions/concentrations should be determined by the end user. |
分 子 量 | 32kDa |
性 狀 | Lyophilized or Liquid |
濃 度 | 1mg/ml |
免 疫 原 | KLH conjugated synthetic peptide derived from human HOGA1 |
亞 型 | IgG |
純化方法 | affinity purified by Protein A |
儲 存 液 | 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol |
保存條件 | Store at -20 °C for one year. Avoid repeated freeze/thaw cycles. The lyophilized antibody is stable at room temperature for at least one month and for greater than a year when kept at -20°C. When reconstituted in sterile pH 7.4 0.01M PBS or diluent of antibody the antibody is stable for at least two weeks at 2-4 °C. |
產品介紹 |
background: DHDPSL is a 327 amino acid mitochondrial protein that catalyzes the last step in the hydroxyproline metabolic pathway. Existing as two alternatively spliced isoforms, DHDPSL is expressed in kidney and liver and is inhibited by divalent cations. Defects in the gene that encode DHDPSL are the cause of primary hyperoxalurea type III (HP3), a disorder of calcium oxalate nephrolithiasis. Patients with HP3 excrete urine with elevated levels of oxalate and L-glycerate. The DHDPSL gene maps to human chromosome 10, which contains over 800 genes and 135 million nucleotides. Defects in some of the genes that map to chromosome 10 are associated with Charcot-Marie Tooth disease, Jackson-Weiss syndrome, Usher syndrome, nonsyndromatic deafness, Wolman’s syndrome, Cowden syndrome, multiple endocrine neoplasia type 2 and porphyria Database links: Entrez Gene: 112817 Human Entrez Gene: 67432 Mouse Omim: 613597 Human SwissProt: Q86XE5 Human SwissProt: Q9DCU9 Mouse Unigene: 180346 Human Unigene: 24196 Mouse Unigene: 13905 Rat Important Note: This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications. |
1、抗體溶解方法 | |
2、抗體修復方式 | |
3、常用試劑的配制 | |
4、免疫組化操作步驟 | |
5、免疫組化問題解答 | |
6、Western Blotting 操作步驟 | |
7、Western Blotting 問題解答 | |
8、關于肽鏈的設計 | |
9、多肽的溶解與保存 | |
10、酶標抗體效價測定程序 | |
| 91丨九色丨熟女丰满 | 成人A片网站发布地址 | 国产精品99朵亚视频免费 | 国产传媒免费在线观看 | 国产人成精品一区二区三 | 成人无码精品一区二区黑寡妇在线 | 狠狠人妻久久久久久综合蜜桃 | 国产AV久久久海角社区 | 嫩草乱码一区三区四区 | A片试看120分钟做受视频红杏 | 波多野结衣在线播放 | 午夜精品久久久久久久99老熟妇 | 蜜臀av黑丝护士人妻少妇诱惑jave | 北条麻妃A片在线播放 | 国产精品无码久久久久一区二区 | 精品一区二区三区蜜桃视频 | 江苏少妇性BBB搡BBB爽爽爽 | 小向美奈子乳巨码在线播放 | 精品国产鲁一鲁一区二区张丽 | 无码区免费看一级毛片A片 免费无码婬片AAAAA片 | 久久精品国产亚洲AV拍拍拍 | 亚洲福利视频首页 | 密桃成人无码人妻一区 | 免费观看理论片A片高清免费观看 | 日韩一区二区三区在线 | 搡老女人老熟女91老熟女综合网 | 亚洲激情视频在线观看 | 精品国产乱码一区二区三区 | 在线观看av的网站 | 亚洲中文字幕人妻少妇 | 97国产精东麻豆人妻电影 | 国产又黄又大又粗视频 | 国产红桃视频精品在线观看 | 特级西西444www大精品视频免费看 | 国产人妻人伦精品熟女A玄幻 | 欧美日韩一区区三区四区 | 亚卅国产乱码在线观看 | 国产精品亚洲日韩AⅤ | 国产传媒在线播放亚洲专区 | 亚洲AV不卡无毒免费在线 |