91精品少妇一区二区三区蜜桃臀,少妇搡BBBB搡BBB搡失恋,BBB片一毛片A片AA少妇,国产成人无码久久久久毛片朴信惠
掃碼關注公眾號           掃碼咨詢技術支持           掃碼咨詢技術服務
  
客服熱線:400-901-9800  客服QQ:4009019800  技術答疑  技術支持  質量反饋  關于我們  聯(lián)系我們
亚洲欧美日韩综合,性一交一乱一A片久久99蜜桃,乱子伦熟妇aVvvzhe汁
首頁 > 產品中心 > 標記一抗 > 產品信息
Rabbit Anti-ETFDH/Gold Conjugated antibody (bs-13110R-Gold)
訂購熱線:400-901-9800
訂購郵箱:sales@bioss.com.cn
訂購QQ:  400-901-9800
技術支持:techsupport@bioss.com.cn
說 明 書: 100ul(10nm  15nm  35nm
100ul/2980.00元
大包裝/詢價
產品編號 bs-13110R-Gold
英文名稱 Rabbit Anti-ETFDH/Gold Conjugated antibody
中文名稱 膠體金標記的電子轉移黃素蛋白脫氫酶抗體
別    名 Electron transfer flavoprotein ubiquinone oxidoreductase; Electron transfer flavoprotein-ubiquinone oxidoreductase; electron transferring flavoprotein dehydrogenase; Electron-transferring-flavoprotein dehydrogenase; ETF dehydrogenase; ETF QO; ETF ubiquinone oxidoreductase; ETF-QO; ETF-ubiquinone oxidoreductase; ETFD_HUMAN; Etfdh; mitochondrial.  
規(guī)格價格 100ul/2980元 購買        大包裝/詢價
說 明 書 100ul(10nm  15nm  35nm
研究領域 細胞生物  信號轉導  細胞類型標志物  新陳代謝  
抗體來源 Rabbit
克隆類型 Polyclonal
交叉反應 (predicted: Human, Mouse, Rat, Chicken, Dog, Horse, Rabbit, )
產品應用 IEM=1:20-200 ICA=1:20-200 ChIP=1:20-200 
not yet tested in other applications.
optimal dilutions/concentrations should be determined by the end user.
分 子 量 65kDa
性    狀 Lyophilized or Liquid
濃    度 0.4mg/ml
免 疫 原 KLH conjugated synthetic peptide derived from human ETFDH
亞    型 IgG
純化方法 affinity purified by Protein A
儲 存 液 0.02M TBS(pH8.2) with 1% BSA, 0.03% Proclin300.
保存條件 Store at 2-8 oC for 3-6 months. Avoid repeated freeze/thaw cycles.
產品介紹 background:
Electron-transferring-flavoprotein dehydrogenase in the inner mitochondrial membrane accepts electrons from electron-transfer flavoprotein which is located in the mitochondrial matrix and reduces ubiquinone in the mitochondrial membrane. The protein is synthesized as a 67-kDa precursor which is targeted to mitochondria and processed in a single step to a 64-kDa mature form located in the mitochondrial membrane. Deficiency in electron-transferring-flavoprotein dehydrogenase have been demonstrated in some patients with type II glutaricacidemia. [provided by RefSeq, Jul 2008].

Function:
Accepts electrons from ETF and reduces ubiquinone.

Subunit:
Monomer.

Subcellular Location:
Mitochondrion inner membrane.

DISEASE:
Defects in ETFDH are the cause of glutaric aciduria type 2C (GA2C) [MIM:231680]. GA2C is an autosomal recessively inherited disorder of fatty acid, amino acid, and choline metabolism. It is characterized by multiple acyl-CoA dehydrogenase deficiencies resulting in large excretion not only of glutaric acid, but also of lactic, ethylmalonic, butyric, isobutyric, 2-methyl-butyric, and isovaleric acids.

Similarity:
Belongs to the ETF-QO/fixC family.
Contains 1 4Fe-4S ferredoxin-type domain.

Database links:
UniProtKB/Swiss-Prot: Q16134.2

Important Note:
This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications.
版權所有 2004-2026 m.rvdoil.com 北京博奧森生物技術有限公司
通過國際質量管理體系ISO 9001:2015 GB/T 19001-2016    證書編號: 00124Q34771R2M/1100
通過國際醫(yī)療器械-質量管理體系ISO 13485:2016 GB/T 42061-2022    證書編號: CQC24QY10047R0M/1100
京ICP備05066980號-1         京公網(wǎng)安備110107000727號
2021人人操人人爱 | 91在线无码精品蜜桃 | 国产精品无呻吟AV无码 | 99免费视频在线观看 | 亚洲春色一区二区三区 | 日本人成A片在线一区二区 人人添人人澡人人爽人人澡 | 国产69久久久欧美黑人A片 | 黄色视频网站在线下载 | 中文字幕免费观看哔哔在线 | 密桃一区二区三区在线观看 | 精品人妻一区二区三区阅读全文 | 911亚洲精品无码成人A片在线 | 亚洲国产精品久久 | 久久精品www人人爽人人 | 四虎地址8848精品 | 寡妇高潮一级寡妇房间 | 国产在线视频在线视 | www.17c.com国产大片 | a激情视频在线观看免费 | 国产一级久久久久毛片精品 | 91少妇人妻偷人网站 | 男女无遮挡XX00动态图120秒 | 波多野结衣无码视频 | 蜜臂AV成人无码久久精品 | 欧美熟妇无码XXXXXX辛迪 | 亚洲中文字幕第一区 | 人妻丰满精品一区二区A片 欧美寡妇性猛交XXX无码 | 亚洲AV无码成人精品区 | 中文字幕永久在线 | 四川少妇XXXⅩ性XXX | 红桃视频成人网站免费进 | 好男人一区二区三区在线观看 | 又粗又大内射免费视频小说 | 久久免费看少妇高潮片A黄 国产AV无码AV高清AV | 成人做爰www免费网站 | 五十路老熟女 码A片 | 亚洲第一页在线观看 | 夜本色视频一区二区三区 | 东京热成人免费播放A片 | 91在线无码精品秘 色 | 精品嫩草AV片导航 |